C96.0
Billable codeMultifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
The ICD-10 code for multifocal and multisystemic (disseminated) langerhans-cell histiocytosis is C96.0.
Clinical notes
Excludes1 (not coded here)
An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Histiocytosis X, multisystemic
- Letterer-Siwe disease
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- C96.2Malignant mast cell neoplasmnon-billable header
- C96.4Sarcoma of dendritic cells (accessory cells)
- C96.5Multifocal and unisystemic Langerhans-cell histiocytosis
- C96.6Unifocal Langerhans-cell histiocytosis
- C96.9Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified
- C96.AHistiocytic sarcoma
- C96.ZOther specified malignant neoplasms of lymphoid, hematopoietic and related tissue
- C96.0Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 20250Approximate match
- 20251Approximate match
- 20252Approximate match
- 20253Approximate match
- 20254Approximate match
- 20255Approximate match
- 20256Approximate match
- 20257Approximate match
- 20258Approximate match
Associated MS-DRGs
C96.0 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.
- DRG 011Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with MCC
- DRG 012Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with CC
- DRG 013Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy without CC/MCC
- DRG 814Reticuloendothelial and Immunity Disorders with MCC
- DRG 815Reticuloendothelial and Immunity Disorders with CC
- DRG 816Reticuloendothelial and Immunity Disorders without CC/MCC
- DRG 826Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with MCC
- DRG 827Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures with CC
- DRG 828Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Major O.R. Procedures without CC/MCC
- DRG 829Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Other Procedures with CC/MCC
- DRG 830Myeloproliferative Disorders or Poorly Differentiated Neoplasms with Other Procedures without CC/MCC
- DRG 843Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses with MCC
- DRG 844Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses with CC
- DRG 845Other Myeloproliferative Disorders or Poorly Differentiated Neoplastic Diagnoses without CC/MCC