D76.1
Billable codeHemophagocytic lymphohistiocytosis
The ICD-10 code for hemophagocytic lymphohistiocytosis is D76.1.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Familial hemophagocytic reticulosis
- Histiocytoses of mononuclear phagocytes
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- D76.2Hemophagocytic syndrome, infection-associated
- D76.3Other histiocytosis syndromes
- D76.1Hemophagocytic lymphohistiocytosis
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 2884Approximate match
Associated MS-DRGs
D76.1 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.