E71.111
Billable code3-methylglutaconic aciduria
The ICD-10 code for 3-methylglutaconic aciduria is E71.111.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E71.110Isovaleric acidemia
- E71.118Other branched-chain organic acidurias
- E71.1113-methylglutaconic aciduria
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 2703Approximate match
Associated MS-DRGs
E71.111 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.