E71.51
Header — not billableDisorders of peroxisome biogenesis
The ICD-10 code for disorders of peroxisome biogenesis is E71.51.
E71.51 is a non-billable header code. It groups related conditions but cannot be used on its own for reimbursement — select one of the 3 more specific codes below.
Clinical notes
Excludes1 (not coded here)
An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).
- Refsum's disease (G60.1)
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Group 1 peroxisomal disorders
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •This is a non-billable header code. Documentation must support a more specific child code before this diagnosis can be reported on a claim.
- •Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E71.50Peroxisomal disorder, unspecified
- E71.52X-linked adrenoleukodystrophynon-billable header
- E71.53Other group 2 peroxisomal disorders
- E71.54Other peroxisomal disordersnon-billable header
- E71.51Disorders of peroxisome biogenesisnon-billable header