E71.541
Billable codeZellweger-like syndrome
The ICD-10 code for zellweger-like syndrome is E71.541.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E71.540Rhizomelic chondrodysplasia punctata
- E71.542Other group 3 peroxisomal disorders
- E71.548Other peroxisomal disorders
- E71.541Zellweger-like syndrome
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 27786Approximate match
Associated MS-DRGs
E71.541 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.