E74.4
Billable codeDisorders of pyruvate metabolism and gluconeogenesis
The ICD-10 code for disorders of pyruvate metabolism and gluconeogenesis is E74.4.
Clinical notes
Excludes1 (not coded here)
An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Deficiency of phosphoenolpyruvate carboxykinase
- Deficiency of pyruvate carboxylase
- Deficiency of pyruvate dehydrogenase
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E74.0Glycogen storage diseasenon-billable header
- E74.1Disorders of fructose metabolismnon-billable header
- E74.2Disorders of galactose metabolismnon-billable header
- E74.3Other disorders of intestinal carbohydrate absorptionnon-billable header
- E74.8Other specified disorders of carbohydrate metabolismnon-billable header
- E74.9Disorder of carbohydrate metabolism, unspecified
- E74.4Disorders of pyruvate metabolism and gluconeogenesis
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 2710Approximate match
- 2718Approximate match
Associated MS-DRGs
E74.4 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.