E77.0
Billable codeDefects in post-translational modification of lysosomal enzymes
The ICD-10 code for defects in post-translational modification of lysosomal enzymes is E77.0.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III [pseudo-Hurler polydystrophy]
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E77.1Defects in glycoprotein degradation
- E77.8Other disorders of glycoprotein metabolism
- E77.9Disorder of glycoprotein metabolism, unspecified
- E77.0Defects in post-translational modification of lysosomal enzymes
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 2727Approximate match
Associated MS-DRGs
E77.0 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.