E79.81
Billable codeAicardi-Goutières syndrome
The ICD-10 code for aicardi-goutières syndrome is E79.81.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E79.82Hereditary xanthinuria
- E79.89Other specified disorders of purine and pyrimidine metabolism
- E79.81Aicardi-Goutières syndrome
Associated MS-DRGs
E79.81 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.