E84.0
Billable codeCystic fibrosis with pulmonary manifestations
The ICD-10 code for cystic fibrosis with pulmonary manifestations is E84.0.
Clinical notes
Use additional code
This code represents an underlying condition. When a related manifestation is also present, coding convention calls for an additional code to be listed after this one.
- code to identify any infectious organism present, such as:
- Pseudomonas (B96.5)
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •If the associated manifestation or related condition noted above is also documented, an additional code should be reported alongside this one.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E84.1Cystic fibrosis with intestinal manifestationsnon-billable header
- E84.8Cystic fibrosis with other manifestations
- E84.9Cystic fibrosis, unspecified
- E84.0Cystic fibrosis with pulmonary manifestations
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 27702
Associated MS-DRGs
E84.0 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.