G90.1
Billable codeFamilial dysautonomia [Riley-Day]
The ICD-10 code for familial dysautonomia [riley-day] is G90.1.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- G90.0Idiopathic peripheral autonomic neuropathynon-billable header
- G90.2Horner's syndrome
- G90.3Multi-system degeneration of the autonomic nervous system
- G90.4Autonomic dysreflexia
- G90.5Complex regional pain syndrome I (CRPS I)non-billable header
- G90.8Other disorders of autonomic nervous systemnon-billable header
- G90.9Disorder of the autonomic nervous system, unspecified
- G90.APostural orthostatic tachycardia syndrome [POTS]
- G90.BLMNB1-related autosomal dominant leukodystrophy
- G90.1Familial dysautonomia [Riley-Day]
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 7428Approximate match
Associated MS-DRGs
G90.1 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.