K00.5
Billable codeHereditary disturbances in tooth structure, not elsewhere classified
The ICD-10 code for hereditary disturbances in tooth structure, not elsewhere classified is K00.5.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Amelogenesis imperfecta
- Dentinogenesis imperfecta
- Odontogenesis imperfecta
- Dentinal dysplasia
- Shell teeth
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- K00.0Anodontia
- K00.1Supernumerary teeth
- K00.2Abnormalities of size and form of teeth
- K00.3Mottled teeth
- K00.4Disturbances in tooth formation
- K00.6Disturbances in tooth eruption
- K00.7Teething syndrome
- K00.8Other disorders of tooth development
- K00.9Disorder of tooth development, unspecified
- K00.5Hereditary disturbances in tooth structure, not elsewhere classified
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 5205
Associated MS-DRGs
K00.5 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.
- DRG 011Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with MCC
- DRG 012Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with CC
- DRG 013Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy without CC/MCC
- DRG 157Dental and Oral Diseases with MCC
- DRG 158Dental and Oral Diseases with CC
- DRG 159Dental and Oral Diseases without CC/MCC