Q04.2
Billable codeHoloprosencephaly
The ICD-10 code for holoprosencephaly is Q04.2.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- Q04.0Congenital malformations of corpus callosum
- Q04.1Arhinencephaly
- Q04.3Other reduction deformities of brain
- Q04.4Septo-optic dysplasia of brain
- Q04.5Megalencephaly
- Q04.6Congenital cerebral cysts
- Q04.8Other specified congenital malformations of brain
- Q04.9Congenital malformation of brain, unspecified
- Q04.2Holoprosencephaly
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 7422Approximate match
Associated MS-DRGs
Q04.2 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.