Q40.0
Billable codeCongenital hypertrophic pyloric stenosis
The ICD-10 code for congenital hypertrophic pyloric stenosis is Q40.0.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Congenital or infantile constriction
- Congenital or infantile hypertrophy
- Congenital or infantile spasm
- Congenital or infantile stenosis
- Congenital or infantile stricture
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- Q40.1Congenital hiatus hernia
- Q40.2Other specified congenital malformations of stomach
- Q40.3Congenital malformation of stomach, unspecified
- Q40.8Other specified congenital malformations of upper alimentary tract
- Q40.9Congenital malformation of upper alimentary tract, unspecified
- Q40.0Congenital hypertrophic pyloric stenosis
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 7505
Associated MS-DRGs
Q40.0 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.
- DRG 314Other Circulatory System Diagnoses with MCC
- DRG 315Other Circulatory System Diagnoses with CC
- DRG 316Other Circulatory System Diagnoses without CC/MCC
- DRG 393Other Digestive System Diagnoses with MCC
- DRG 394Other Digestive System Diagnoses with CC
- DRG 395Other Digestive System Diagnoses without CC/MCC